Pharmacogenomics · Pharmacology

Which genetic variation is linked to an increased risk of 'Torsades de Pointes' when taking QT-prolonging drugs?

  1. Congenital long QT syndrome mutations
  2. CYP3A4 gene over-expression
  3. Alpha-1 antitrypsin deficiency
  4. Hereditary hemochromatosis gene mutations
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Correct answer: Congenital long QT syndrome mutations

Mutations in cardiac ion channel genes can cause subclinical Long QT Syndrome. When these patients take drugs that further block potassium channels (like certain antiarrhythmics or antibiotics), they are at high risk for fatal arrhythmias.

Difficulty: Medium Question 18 of 20

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