Congenital Heart Defects in Children · NCLEX Exam

A child with a fenestrated Fontan procedure for single-ventricle physiology is most at risk for which long-term complication?

  1. Spontaneous closure of the fenestration without consequence
  2. Liver congestion/ fibrosis, arrhythmias, thromboembolism
  3. No complications once procedure is done
  4. Increased systemic blood flow to lungs only
Show answer and explanation

Correct answer: Liver congestion/ fibrosis, arrhythmias, thromboembolism

Fontan circulation places systemic venous return directly into pulmonary arteries; over time this may cause liver fibrosis, arrhythmias and thromboembolic events.

Difficulty: Medium Question 11 of 14

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