A patient with an inborn error of metabolism affecting carbohydrate storage presents with severe fasting hypoglycemia and lactic acidosis. Which category does this most likely belong to?
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Correct answer: Glycogen storage disease (glycogen metabolism disorder)
Glycogen storage diseases affect the ability to mobilize stored glycogen during fasting; impaired glycogenolysis or gluconeogenesis can lead to hypoglycemia and lactic acidosis.
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