Multiple Endocrine Neoplasia · Pathology

Which feature distinguishes MEN2B from MEN2A?

  1. Presence of parathyroid hyperplasia
  2. Mucosal neuromas and marfanoid habitus
  3. Pituitary adenomas
  4. Pancreatic neuroendocrine tumors
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Correct answer: Mucosal neuromas and marfanoid habitus

MEN2B is characterized by mucosal neuromas and a marfanoid body habitus, in addition to medullary thyroid carcinoma and pheochromocytoma. Parathyroid involvement is uncommon in MEN2B.

Difficulty: Medium Question 6 of 20

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