A child with ARPKD develops portal hypertension and splenomegaly. This is most likely due to:
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Correct answer: Congenital hepatic fibrosis linked to the disease
ARPKD is associated with congenital hepatic fibrosis, leading to portal hypertension, splenomegaly, and liver complications.
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More Congenital Kidney Disorders questions
- Which feature is more characteristic of ADPKD rather than ARPKD?
- In a patient with a congenital duplex collecting system, the major risk the nurse should monitor for is:
- What finding on ultrasound is most consistent with early ADPKD in an adult with a positive family history?
- In an infant with suspected ARPKD, which antenatal ultrasound finding would raise concern?
- Which statement about the genetic transmission of ADPKD is correct?
- Which of these is not typically a complication of PKD?